Material and Methods: We assessed the etiological factors, diagnosis and treatment, pathologic findings, follow-up and results after treatment in the patient with a desmoid tumor.

Results: Initially, an abdominal ultrasonography was performed. A solid mass in the rectus muscle with a 24-12 mm diameter was observed. The patient is operated. The tumor is removed widely, together with the adjacent uninvolved tissues about 2 cm. Abdominal wall layers were closed conveniently. In the pathological evaluation, it was observed that the fibroblasts had destructed and atrophied the muscle fibrillae. Any postoperative complication or local recurrence was not seen in the long-term follow-up (108 months).

Conclusion: The first line therapy is radical surgical resection in desmoid tumors which are seen rarely, particularly in childbearing women and have local invasive characteristics. Local recurrence does not usually occur in tumors which are resected with sufficient surgical margins.